nodgoРоссийский журнал детской гематологии и онкологии (РЖДГиО)Russian Journal of Pediatric Hematology and Oncology2311-12672413-5496LTD “Graphica”10.21682/2311-1267-2025-12-1-48-54nodgo-1130Research ArticleОБЗОРЫ ЛИТЕРАТУРЫLITERATURE REVIEWSПервичные злокачественные опухоли легких у детей (обзор литературы)Primary malignant lung tumors in children (review of the literature)https://orcid.org/0000-0001-9424-1646УсковаН. Г.UskovaN. G.

Наталья Геннадьевна Ускова - к.м.н., врач-детский хирург отделения онкологии и детской хирургии, старший научный сотрудник отдела торакоабдоминальной хирургии 

117997, Москва, ул. Саморы Машела, 1

Cand. of Sci (Med.), Pediatric Surgeon Department of Oncology and Pediatric Surgery, Senior Researcher Department of Thoracoabdominal Surgery

1 Samory Mashela St., Moscow, 117997

nataliya.uskova@dgoi.ruhttps://orcid.org/0000-0002-1387-209XАхаладзеД. Г.AkhaladzeD. G.

д.м.н., заместитель главного врача по хирургии, заведующий отделом торакоабдоминальной хирургии 

117997, Москва, ул. Саморы Машела, 1

Dr. of Sci. (Med.), Deputy Chief Physician for Surgery, Head of the Department of Thoracoabdominal Surgery

1 Samory Mashela St., Moscow, 117997

dmitry.ahaladze@dgoi.ruhttps://orcid.org/0000-0002-4451-3233ГрачевН. С.GrachevN. S.

д.м.н., профессор, генеральный директор

117997, Москва, ул. Саморы Машела, 1

Dr. of Sci. (Med.), Professor, General Directorat 

1 Samory Mashela St., Moscow, 117997

nikolay.grachev@dgoi.ruФГБУ «НМИЦ ДГОИ им. Дмитрия Рогачева» Минздрава РоссииРоссияDmitry Rogachev National Medical Research Center of Pediatric Hematology, Oncology and Immunology, Ministry of Health of RussiaRussian Federation2025230420251214854Copyright © Ускова Н.Г., Ахаладзе Д.Г., Грачев Н.С., 20252025Ускова Н.Г., Ахаладзе Д.Г., Грачев Н.С.Uskova N.G., Akhaladze D.G., Grachev N.S.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://journal.nodgo.org/jour/article/view/1130

Первичные злокачественные опухоли легких – крайне редко встречающаяся в детском и подростковом возрасте патология.

Цель данной публикации – обзор наиболее полных и весомых ретроспективных исследований, посвященных данной нозологии, изучение эпидемиологии, клинической картины и методов лечения, а также оценка прогноза по заболеванию в зависимости от гистологического типа опухоли.

Primary malignant lung tumors are an extremely rare pathology in childhood and adolescents.

The purpose of this publication – is to review the most complete and significant retrospective studies on this pathology, to explore the epidemiology, clinical symptoms and treatment methods, as well as to assess the prognosis of the disease depending on the histological type of tumor.

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The authors declare that there are no conflicts of interest present.