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<article article-type="research-article" dtd-version="1.3" xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance" xml:lang="ru"><front><journal-meta><journal-id journal-id-type="publisher-id">nodgo</journal-id><journal-title-group><journal-title xml:lang="ru">Российский журнал детской гематологии и онкологии (РЖДГиО)</journal-title><trans-title-group xml:lang="en"><trans-title>Russian Journal of Pediatric Hematology and Oncology</trans-title></trans-title-group></journal-title-group><issn pub-type="ppub">2311-1267</issn><issn pub-type="epub">2413-5496</issn><publisher><publisher-name>LTD “Graphica”</publisher-name></publisher></journal-meta><article-meta><article-id pub-id-type="doi">10.17650/2311-1267-2017-4-1-77-80</article-id><article-id custom-type="elpub" pub-id-type="custom">nodgo-285</article-id><article-categories><subj-group subj-group-type="heading"><subject>Research Article</subject></subj-group><subj-group subj-group-type="section-heading" xml:lang="ru"><subject>ВОПРОСЫ ПРАКТИЧЕСКОЙ ГЕМАТОЛОГИИ-ОНКОЛОГИИ</subject></subj-group><subj-group subj-group-type="section-heading" xml:lang="en"><subject>QUESTIONS OF PRACTICAL HEMATOLOGY/ONCOLOGY</subject></subj-group></article-categories><title-group><article-title>Современные аспекты диагностики и лечения патологии гемостаза на основе опыта французского центра</article-title><trans-title-group xml:lang="en"><trans-title>Modern aspects of diagnosis and treatment of diseases of hemostasis based on the French center experience</trans-title></trans-title-group></title-group><contrib-group><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Федорова</surname><given-names>Д. В.</given-names></name><name name-style="western" xml:lang="en"><surname>Fedorova</surname><given-names>D. V.</given-names></name></name-alternatives><bio xml:lang="ru"><p>117997, Москва, ул. Саморы Машела, 1</p></bio><bio xml:lang="en"><p>1 Samory Mashela St., Moscow, 117997</p></bio><email xlink:type="simple">darya.v.fedorova@gmail.com</email><xref ref-type="aff" rid="aff-1"/></contrib></contrib-group><aff-alternatives id="aff-1"><aff xml:lang="ru"><institution>ФГБУ «ННПЦ ДГОИ им. Дмитрия Рогачева» Минздрава России</institution><country>Россия</country></aff><aff xml:lang="en"><institution>Dmitry Rogachev National Research Center of Pediatric Hematology, Oncology and Immunology, Ministry of Health of Russia</institution><country>Russian Federation</country></aff></aff-alternatives><pub-date pub-type="collection"><year>2017</year></pub-date><pub-date pub-type="epub"><day>01</day><month>03</month><year>2017</year></pub-date><volume>4</volume><issue>1</issue><fpage>77</fpage><lpage>80</lpage><permissions><copyright-statement>Copyright &amp;#x00A9; Федорова Д.В., 2017</copyright-statement><copyright-year>2017</copyright-year><copyright-holder xml:lang="ru">Федорова Д.В.</copyright-holder><copyright-holder xml:lang="en">Fedorova D.V.</copyright-holder><license xml:lang="ru" license-type="creative-commons-attribution" xlink:href="https://creativecommons.org/licenses/by/4.0/" xlink:type="simple"><license-p>Данная работа распространяется под лицензией Creative Commons Attribution 4.0.</license-p></license><license xml:lang="en" license-type="creative-commons-attribution" xlink:href="https://creativecommons.org/licenses/by/4.0/" xlink:type="simple"><license-p>This work is licensed under a Creative Commons Attribution 4.0 License.</license-p></license></permissions><self-uri xlink:href="https://journal.nodgo.org/jour/article/view/285">https://journal.nodgo.org/jour/article/view/285</self-uri><abstract><p>В настоящее время проблема тромбоцитопений и тромбоцитопатий, а также патология гемостаза в целом является важным вопросом, который представляет собой интересную тему, актуальную для всех детских гематологов и онкологов. Одним из лидеров направления в изучении данного вопроса является Госпиталь Тимон в г. Марсель (Франция), передовой опыт которого представлен в статье победителя конкурса на лучшее представление клинического случая, проводимого Национальным обществом детских гематологов и онкологов.</p></abstract><trans-abstract xml:lang="en"><p>Now the problem thrombocytopenia and thrombocytopathy and pathology of hemostasis in general is an important issue, which is an interesting topic, relevant for all children’s hematology and oncology. One of the leading trends in the study of this issue is Timon Hospital in Marseilles (France), of which the best practices presented in the article, the winner for the best presentation of clinical cases, held by the National Society of Pediatric Hematology and Oncology.</p></trans-abstract><kwd-group xml:lang="ru"><kwd>дети</kwd><kwd>тромбоцитопении</kwd><kwd>тромбоцитопатии</kwd><kwd>новые технологии</kwd></kwd-group><kwd-group xml:lang="en"><kwd>children</kwd><kwd>thrombocytopenia</kwd><kwd>thrombocytopathy</kwd><kwd>new technologies</kwd></kwd-group></article-meta></front><back><ref-list><title>References</title><ref id="cit1"><label>1</label><citation-alternatives><mixed-citation xml:lang="ru">Gresele P.; Subcommittee on Platelet Physiology of the International Society on Thrombosis and Hemostasis. Diagnosis of inherited platelet function disorders: guidance from the SSC of the ISTH. 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