nodgoРоссийский журнал детской гематологии и онкологии (РЖДГиО)Russian Journal of Pediatric Hematology and Oncology2311-12672413-5496LTD “Graphica”10.17650/2311-1267-2018-5-1-87-94nodgo-364Research ArticleСЛУЧАЙ ИЗ ПРАКТИКИCASE STUDYАнгиоматоидная фиброзная гистиоцитома у детей: описание клинического случая и обзор литературыAngiomatoid fibrous histiocytoma in children: case report and the review of literatureБурголМ. М.BurgolM. M.

Мария Михайловна Бургол 

117997, Москва, ул. Саморы Машела, 1 

mariyaburgol@gmail.comКачановД. Ю.KachanovD. Yu.

117997, Москва, ул. Саморы Машела, 1 

РощинВ. Ю.RoshchinV. Yu.

117997, Москва, ул. Саморы Машела, 1 

СулеймановаА. М.SuleymanovaA. M.

117997, Москва, ул. Саморы Машела, 1 

МеркуловН. Н.MerkulovN. N.

117997, Москва, ул. Саморы Машела, 1 

КазаковаА. Н.KazakovaA. N.

117997, Москва, ул. Саморы Машела, 1 

ЩербаковА. П.ShcherbakovA. P.

117997, Москва, ул. Саморы Машела, 1 

ТерещенкоГ. В.TereshchenkoG. V.

117997, Москва, ул. Саморы Машела, 1 

ШаманскаяТ. В.ShamanskayaT. V.

117997, Москва, ул. Саморы Машела, 1 

ВарфоломееваС. Р.VarfolomeevaS. R.

117997, Москва, ул. Саморы Машела, 1 

ФГБУ «Национальный медицинский исследовательский центр детской гематологии, онкологии и иммунологии им. Дмитрия Рогачева» Минздрава РоссииРоссияDmitry Rogachev National Medical Research Center of Pediatric Hematology, Oncology and Immunology, Ministry of Health of RussiaRussian Federation201820022018518794Copyright © Бургол М.М., Качанов Д.Ю., Рощин В.Ю., Сулейманова А.М., Меркулов Н.Н., Казакова А.Н., Щербаков А.П., Терещенко Г.В., Шаманская Т.В., Варфоломеева С.Р., 20182018Бургол М.М., Качанов Д.Ю., Рощин В.Ю., Сулейманова А.М., Меркулов Н.Н., Казакова А.Н., Щербаков А.П., Терещенко Г.В., Шаманская Т.В., Варфоломеева С.Р.Burgol M.M., Kachanov D.Y., Roshchin V.Y., Suleymanova A.M., Merkulov N.N., Kazakova A.N., Shcherbakov A.P., Tereshchenko G.V., Shamanskaya T.V., Varfolomeeva S.R.This work is licensed under a Creative Commons Attribution 4.0 License.https://journal.nodgo.org/jour/article/view/364

Ангиоматоидная фиброзная гистиоцитома (АФГ) является чрезвычайно редкой опухолью мягких тканей у детей, характеризующейся промежуточным биологическим поведением. В настоящей статье представлено описание случая АФГ с поражением мягких тканей поясничной области у ребенка 10 лет. Даны современные данные об эпидемиологии, молекулярной генетике, особенностях диагностики и лечения АФГ у детей. 

Angiomatoid fibrous histiocytoma (AFH) is an extremely rare soft tissue tumor in children characterized by intermediate biological behavior. This article describes a case of AFH of soft tissue of the lumbar region in 10-year-old child. The literature review describes the state-of-the-art data on epidemiology, molecular genetics, diagnostics and treatment of AFH in children. 

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The authors declare that there are no conflicts of interest present.