nodgoРоссийский журнал детской гематологии и онкологии (РЖДГиО)Russian Journal of Pediatric Hematology and Oncology2311-12672413-5496LTD “Graphica”10.21682/2311-1267-2022-9-3-90-92nodgo-862Research ArticleКЛИНИЧЕСКИЕ НАБЛЮДЕНИЯCLINICAL CASESПриобретенная гемофилия А с внутримышечной гематомой в необычном возрасте: клинический случайAcquired hemophilia A with intramuscular hematoma at an unusual age: a case reporthttps://orcid.org/0000-0002-4320-7509NourbakhshS.M.K.NourbakhshS.M.K.

Department of Pediatric Hematology and Oncology, Imam Khomeini Hospital Complex

Keshavarz Blvd., Tehran, Iran 14197-33141

Seyed Mohammad Kazem Nourbakhsh: MD, Associate Professor of Pediatric Hematology and Oncology, Department of Pediatric Hematology and Oncology, Imam Khomeini Hospital Complex

Keshavarz Blvd., Tehran, 14197-33141

dr.nourbakhsh2010@gmail.comhttps://orcid.org/0000-0002-7106-9799BahadoramM.BahadoramM.

Thalassemia and Hemoglobinopathy Research Center

Golestan St., Ahvaz, Iran 15794–61357

Bahadoram Mohammad: MD, Researcher, Thalassemia and Hemoglobinopathy Research Center

Golestan St., Ahvaz, 15794–61357

mohammadbahadoram@yahoo.comhttps://orcid.org/0000-0002-7151-4805EskandarionS.EskandarionS.

Department of Pediatric Hematology and Oncology, Imam Khomeini Hospital Complex

Keshavarz Blvd., Tehran, Iran 14197-33141

Sahar Eskandarion: MD, Pediatrician, Department of Pediatric Hematology and Oncology, Imam Khomeini Hospital Complex

Keshavarz Blvd., Tehran, 14197-33141

Sahar.eskandarion@tums.ac.irhttps://orcid.org/0000-0002-5091-5191HassanzadehS.HassanzadehS.

Thalassemia and Hemoglobinopathy Research Center

Golestan St., Ahvaz, Iran 15794–61357

Shakiba Hassanzadeh: MD, Researcher, Thalassemia and Hemoglobinopathy Research Center

Golestan St., Ahvaz, 15794–61357

shak.hassanzadeh@gmail.comTehran University of Medical SciencesИранTehran University of Medical SciencesIslamic Republic of IranHealth Research Institute, Ahvaz Jundishapur University of Medical SciencesИранHealth Research Institute, Ahvaz Jundishapur University of Medical SciencesIslamic Republic of Iran202209112022939092Copyright © Nourbakhsh S., Bahadoram M., Eskandarion S., Hassanzadeh S., 20222022Nourbakhsh S., Bahadoram M., Eskandarion S., Hassanzadeh S.Nourbakhsh S., Bahadoram M., Eskandarion S., Hassanzadeh S.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://journal.nodgo.org/jour/article/view/862

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Background

Background. Acquired factor VIII (FVIII) deficiency or acquired hemophilia A (AHA) is very uncommon in children. Patients with AHA usually present with abnormal or unexpected bleeding which may be life-threatening. These patients usually have unexplained, prolonged, and isolated activated partial thromboplastin time (aPTT). Consequently, FVIII activity should be immediately evaluated. Bleeding prevention is important in patients with AHA.

Case report

Case report. We present a case of a previously healthy 13-year-old female who presented with intramuscular hematoma, soft tissue hemorrhage, and epistaxis who was eventually diagnosed with AHA.

Conclusion

Conclusion. To our knowledge, the present report is one of the few reported cases of an Asian patient that was diagnosed with acquired hemophilia A at a young age.

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The authors declare that there are no conflicts of interest present.