Congenital infantile fibrosarcoma of soft tissues of the chest wall on the left (description of the clinical case and literature review)
G. B. Sagoyan,
M. V. Rubanskaya,
P. A. Kerimov,
O. A. Kapkova,
M. A. Rubanskiy,
D. V. Shevtsov,
A. M. Suleymanova,
R. I. Pimenov,
A. S. Temnyy,
N. V. Matinyan,
E. V. Mikhailova,
A. P. Kazantsev,
S. R. Varfolomeeva https://doi.org/10.21682/2311-1267-2020-7-1-75-81
Abstract
Infantile fibrosarcoma (IF) is a rare soft tissue sarcoma that occurs with a frequency of 1% of all cases of malignant neoplasms in children in the first year of life. IF most often affects the soft tissues of the upper and lower extremities. Rare localizations include the trunk, the head and neck, and the gastrointestinal tract. The article describes a rare clinical case of congenital IF of soft tissues of the chest wall in a newborn, as well as a literature review.
About the Authors
G. B. Sagoyan
Research Institute of Pediatric Oncology and Hematology of N.N. Blokhin National Medical Research Centre of Oncology, Ministry of Health of Russia
Russian Federation
Russian Federation
Pediatric Oncologist
SPIN-code: 6304-0159
23 Kashirskoe Shosse, Moscow, 115478, Russia
M. V. Rubanskaya
Research Institute of Pediatric Oncology and Hematology of N.N. Blokhin National Medical Research Centre of Oncology, Ministry of Health of Russia
Russian Federation
Russian Federation
Cand. of Sci. (Med.), Researcher and Pediatric Oncologist Department of Surgery No. 2
23 Kashirskoe Shosse, Moscow, 115478, Russia
P. A. Kerimov
Research Institute of Pediatric Oncology and Hematology of N.N. Blokhin National Medical Research Centre of Oncology, Ministry of Health of Russia
Russian Federation
Russian Federation
Dr. of Sci. (Med.), Leading Researcher Department of Surgery No. 2
23 Kashirskoe Shosse, Moscow, 115478, Russia
O. A. Kapkova
Research Institute of Pediatric Oncology and Hematology of N.N. Blokhin National Medical Research Centre of Oncology, Ministry of Health of Russia
Russian Federation
Russian Federation
Pediatric Oncologist Department of Surgery No. 2
23 Kashirskoe Shosse, Moscow, 115478, Russia
M. A. Rubanskiy
Research Institute of Pediatric Oncology and Hematology of N.N. Blokhin National Medical Research Centre of Oncology, Ministry of Health of Russia
Russian Federation
Russian Federation
Cand. of Sci. (Med.), Pediatric Surgeon Department of Surgery No. 2
23 Kashirskoe Shosse, Moscow, 115478, Russia
D. V. Shevtsov
Research Institute of Pediatric Oncology and Hematology of N.N. Blokhin National Medical Research Centre of Oncology, Ministry of Health of Russia
Russian Federation
Russian Federation
Pediatric Oncologist Department of Surgery No. 2
23 Kashirskoe Shosse, Moscow, 115478, Russia
A. M. Suleymanova
Research Institute of Pediatric Oncology and Hematology of N.N. Blokhin National Medical Research Centre of Oncology, Ministry of Health of Russia
Russian Federation
Russian Federation
Pediatric Oncologist
23 Kashirskoe Shosse, Moscow, 115478, Russia
R. I. Pimenov
Research Institute of Pediatric Oncology and Hematology of N.N. Blokhin National Medical Research Centre of Oncology, Ministry of Health of Russia
Russian Federation
Russian Federation
Pediatric Oncologist Department of Surgery No. 2
23 Kashirskoe Shosse, Moscow, 115478, Russia
A. S. Temnyy
Research Institute of Pediatric Oncology and Hematology of N.N. Blokhin National Medical Research Centre of Oncology, Ministry of Health of Russia
Russian Federation
Russian Federation
Pediatric Surgeon Department of Surgery No. 2
23 Kashirskoe Shosse, Moscow, 115478, Russia
N. V. Matinyan
Research Institute of Pediatric Oncology and Hematology of N.N. Blokhin National Medical Research Centre of Oncology, Ministry of Health of Russia
Russian Federation
Russian Federation
Dr. of Sci. (Med.), Head of the Department of Anesthesiology and Resuscitatio; Professor Department of Pediatric Anesthesiology and Intensive Care of the N.I. Pirogov Russian National Research Medical University, Ministry of Health of Russia
23 Kashirskoe Shosse, Moscow, 115478, Russia
E. V. Mikhailova
Research Institute of Pediatric Oncology and Hematology of N.N. Blokhin National Medical Research Centre of Oncology, Ministry of Health of Russia
Russian Federation
Russian Federation
Cand. of Sci. (Med.), Head of the Department of Radiology of the Department of Radiation Methods for the Diagnosis and Treatment of Tumors
SPIN-code: 2880-1263
23 Kashirskoe Shosse, Moscow, 115478, Russia
A. P. Kazantsev
Research Institute of Pediatric Oncology and Hematology of N.N. Blokhin National Medical Research Centre of Oncology, Ministry of Health of Russia
Russian Federation
Russian Federation
Dr. of Sci. (Med.), Head of the Department of Surgery No. 2
23 Kashirskoe Shosse, Moscow, 115478, Russia
S. R. Varfolomeeva
Research Institute of Pediatric Oncology and Hematology of N.N. Blokhin National Medical Research Centre of Oncology, Ministry of Health of Russia
Russian Federation
Russian Federation
Dr. of Sci. (Med.), Professor, Deputy Director for Research and Clinical Work – Director of the Research Institute of Pediatric Oncology and Hematology of N.N. Blokhin National Medical Research Center of Oncology, Ministry of Health of Russia, Executive Director of Regional Public Organization National Society of Pediatric Hematologists and Oncologists
23 Kashirskoe Shosse, Moscow, 115478, Russia
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Review
For citations:
Sagoyan G.B., Rubanskaya M.V., Kerimov P.A., Kapkova O.A., Rubanskiy M.A., Shevtsov D.V., Suleymanova A.M., Pimenov R.I., Temnyy A.S., Matinyan N.V., Mikhailova E.V., Kazantsev A.P., Varfolomeeva S.R. Congenital infantile fibrosarcoma of soft tissues of the chest wall on the left (description of the clinical case and literature review). Russian Journal of Pediatric Hematology and Oncology. 2020;7(1):75-81. (In Russ.) https://doi.org/10.21682/2311-1267-2020-7-1-75-81
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