Thrombocytopathy
https://doi.org/10.17650/2311-1267-2015-1-54-60
Abstract
The article is devoted to general issues of classification and differential diagnosis of thrombocytopathy. Features of pathogenesis, clinical course and diagnosis of certain rare inherited thrombocytopathies are highlighted. Particular attention is paid to the formation of the molecular basis of these diseases. The basic genetic mutations associated with a number of thrombocytopathies are given.
About the Authors
I. A. Demina
Federal Research Center of Pediatric Hematology, Oncology and Immunology named after Dmitriy Rogachev, Ministry of Health of Russia
Russian Federation
1 Samory Mashela St., Moscow, 117198, Russia
Russian Federation
1 Samory Mashela St., Moscow, 117198, Russia
M. A. Kumskova
Federal Research Center of Pediatric Hematology, Oncology and Immunology named after Dmitriy Rogachev, Ministry of Health of Russia
Russian Federation
1 Samory Mashela St., Moscow, 117198, Russia
Russian Federation
1 Samory Mashela St., Moscow, 117198, Russia
M. A. Panteleev
Federal Research Center of Pediatric Hematology, Oncology and Immunology named after Dmitriy Rogachev, Ministry of Health of Russia;
Hematological Research Center, Ministry of Health of Russia;
Theoretical Problems Center of Physical and Chemical Pharmacology, Russian Academy of Sciences;
M.V. Lomonosov Moscow State University
Russian Federation
Russian Federation
1 Samory Mashela St., Moscow, 117198, Russia;
4a Novo-Zykovskiy Pr-d, Moscow, 125167, Russia;
38A, Bldg. 1, Leninskiy Prosp., Moscow, 119991, Russia;
1, Bldg. 8 Leninskie Gory St., Moscow, 119234, Russia
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Review
For citations:
Demina I.A., Kumskova M.A., Panteleev M.A. Thrombocytopathy. Russian Journal of Pediatric Hematology and Oncology. 2015;2(1):54-60. (In Russ.) https://doi.org/10.17650/2311-1267-2015-1-54-60
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