Right extended hepatectomy with hepatocaval confluence resection in a 4-year-old child with hepatoblastoma. Clinical case

Tumor thrombosis of the main vessels is a rare complication of malignant neoplasms in children. In the world literature, a few clinical cases of thrombosis of the main vessels in hepatoblastoma are noted. This poses questions to the surgeon, the solution of which does not have a single and standardized approach, as well as sufficient clinical experience in pediatric practice. Treatment of patients with such complications requires careful preparation, planning and coordinated work of an interdisciplinary team of specialists. This article presents a clinical case of a child with right liver lobe hepatoblastoma with tumor-associated thrombosis of the right hepatic vein and inferior vena cava, extending to the right atrium. After neoadjuvant chemotherapy, the patient underwent right extended hepatectomy with resection of the inferior vena cava at the level of hepaticocaval confluence and subsequent reconstruction using an autogenic patch.

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