Case of congenital adrenocortical cancer
https://doi.org/10.21682/2311-1267-2019-6-2-76-79
Abstract
The article presents a unique clinical observation of adrenocortical cancer (ACC) in a newborn baby, whose mother suffered from a recurrent form of maxillary fibrosarcoma and had a burdened obstetric and gynecological history, but was not examined by a geneticist. Complications of ACC in the presented patient were secondary hypertrophic cardiomyopathy with obstruction of the exit paths of both ventricles, Itsenko– Cushing syndrome. Despite the surgical treatment carried out according to vital indications (tumoradinectomy on the right with hormonal support with a Solu-Cortef), the child died during the progression of multiple organ failure and sepsis.
About the Authors
L. R. Karaseva
Nizhny Novgorod Regional Children’s Clinical Hospital;
Privolzhsky Research Medical University, Ministry of Health of Russia
Russian Federation
Russian Federation
Cand. of Sci. (Med.), Physician of Oncology Department Nizhny Novgorod Regional Children’s Clinical Hospital, Docent Department of Pediatric Surgery of the Privolzhsky Research Medical University
211 Vaneeva St., Nizhny Novgorod, 603136; 10/ 1 Minin and Pozharsky Square, Nizhny Novgorod, 603005
L. P. Privalova
Nizhny Novgorod Regional Children’s Clinical Hospital
Russian Federation
Russian Federation
Head of Oncology Department
211 Vaneeva St., Nizhny Novgorod, 603136
E. G. Novopoltseva
Privolzhsky Research Medical University, Ministry of Health of Russia
Russian Federation
Russian Federation
Dr. of Sci. (Med.), Docent, Professor of Department of Pediatrics
10/ 1 Minin and Pozharsky Square, Nizhny Novgorod, 603005
V. V. Radovsky
Nizhny Novgorod Regional Children’s Clinical Hospital
Russian Federation
Russian Federation
Physician of Pathoanatomical Department
211 Vaneeva St., Nizhny Novgorod, 603136
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Review
For citations:
Karaseva L.R., Privalova L.P., Novopoltseva E.G., Radovsky V.V. Case of congenital adrenocortical cancer. Russian Journal of Pediatric Hematology and Oncology. 2019;6(2):76-79. (In Russ.) https://doi.org/10.21682/2311-1267-2019-6-2-76-79
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