Three-stage cytopenia in a child with congenital cavernous transformation of the portal vein
https://doi.org/10.17650/2311-1267-2018-5-3-108-114
Abstract
The article represents a case of observation the patient aged 1 year 9 months with an isolated thrombocytopenia with a drop in platelets to 98 thousand/μL, that had been progressed during 1 year to three-stage cytopenia, which was the result of a congenital cavernous transformation of the portal vein. The differential diagnosis of young children’s cytopenia is a complex clinical task, which can be followed by errors in the diagnosis and, accordingly, the choice of therapy. The care of clinicians regarding only hematological pathology can lead to the confusion. The absence of clinical manifestations and moderate deviations in the hemogram (Hb – 98 g/l, RBC– 4.64 × 1012/l, PLT – 98 × 109/l, WBC – 5.0 × 109/l, GR – 0.79 × 109/l) made the diagnostic search rather difficult in this case.
About the Authors
M. E. Lokhmatova
Dmitry Rogachev National Medical Research Center of Pediatric Hematology, Oncology and Immunology, Ministry of Health of Russia
Russian Federation
Russian Federation
1 Samory Mashela St., Moscow, 117997
I. O. Taishikhina
Dmitry Rogachev National Medical Research Center of Pediatric Hematology, Oncology and Immunology, Ministry of Health of Russia
Russian Federation
Russian Federation
1 Samory Mashela St., Moscow, 117997
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Review
For citations:
Lokhmatova M.E., Taishikhina I.O. Three-stage cytopenia in a child with congenital cavernous transformation of the portal vein. Russian Journal of Pediatric Hematology and Oncology. 2018;5(3):108-114. (In Russ.) https://doi.org/10.17650/2311-1267-2018-5-3-108-114
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