Retinoblastoma with extraocular extension on the optic nerve: the case report

Introduction. Retinoblastoma (Rb) is a rare intraocular tumor, which predominantly occurs in young children. The number of scientific studies and research, dedicated to extraocular Rb with extension on the optic nerve is limited. There is no uniform opinion on how to choose place and method on the surgical phase of treatment for patients with tumor’s extension on the optic nerve.

Description of the case report. The article presents the clinical case of extraocular Rb with extension on the optic nerve in a patient at the age of 5years 1 month. After 3 courses of polychemotherapy a one-stage sequential operation was performed, namely, prechiasmal resection of the optic nerve with eye enucleation. Radiation therapy and adjuvant therapy was carried out in the postoperative period. It was decided to abstain from performing high-dosed chemotherapy. The disease-free observation period from the end of treatment is 6.5 years.

Conclusion. In view of the lack of sufficient experience in treating patients with extraocular Rb, due to the small number of studies in this section of oncology, we were interested to present this clinical case with an emphasis on the surgical stage which has positively influenced the outcome of the disease.

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