Synovial sarcoma of the median nerve of the right shoulder (case report)
https://doi.org/10.21682/2311-1267-2023-10-1-68-72
Abstract
Synovial sarcoma (SS) is a soft tissue tumor that occurs among a group of tumors other than rhabdomyosarcoma (RMS) in childhood and adolescence in 4 % of cases. In terms of incidence among children, SS is second only to RMS and most often occurs in young and mature patients (15–35 years), with a slight predominance in men. The localization of SS in the soft tissues of the extremities reaches 80 %; to a lesser extent, these tumors occur in the head and neck, trunk, retroperitoneal space, and joints (no more than 5 %). Cases of the appearance of SS in the mediastinum, peripheral nerves, skin and visceral organs are also described.
This article presents a rare clinical case of the development of SS of the median nerve of the right shoulder in a 15-year-old patient.
About the Authors
D. B. KhestanovRussian Federation
Cand. of Sci. (Med.), Senior Researcher of the Pediatric Oncology Department of Surgical Methods of Treatment No. 2 (Tumors of Thoracoabdominal Localization and Musculoskeletal System) of the Research Institute of Pediatric Oncology and Hematology named after Academician of the Russian Academy of Medical Sciences L.A. Durnov
23 Kashirskoe Shosse, Moscow, 115522
M. M. Efimova
Russian Federation
Pediatric Oncologist Pediatric Oncology Department No. 2 (Chemotherapy of Tumors of the Musculoskeletal System) of the Research Institute of Pediatric Oncology and Hematology named after Academician of the Russian Academy of Medical Sciences L.A. Durnov
23 Kashirskoe Shosse, Moscow, 115522
O. M. Romantsova
Russian Federation
Pediatric Oncologist, Head of the Department No. 2 (Chemotherapy of Tumors of the Musculoskeletal System) of the Research Institute of Pediatric Oncology and Hematology named after Academician of the Russian Academy of Medical Sciences L.A. Durnov
23 Kashirskoe Shosse, Moscow, 115522
V. V. Khairullova
Russian Federation
Pediatric Oncologist Pediatric Oncology Department No. 2 (Chemotherapy of Tumors of the Musculoskeletal System) of the Research Institute of Pediatric Oncology and Hematology named after Academician of the Russian Academy of Medical Sciences L.A. Durnov
23 Kashirskoe Shosse, Moscow, 115522
A. A. Malakhova
Russian Federation
Head of the Organizational and Methodological Department with the Cancer Register and the Medical Archive of the Research Institute of Pediatric Oncology and Hematology named after Academician of the Russian Academy of Medical Sciences L.A. Durnov
23 Kashirskoe Shosse, Moscow, 115522
E. V. Mikhailova
Russian Federation
Cand. of Sci. (Med.), Head of the Department of Radiology of the Department of Radiation Methods for the Diagnosis and Treatment of Tumors of the Research Institute of Pediatric Oncology and Hematology named after Academician of the Russian Academy of Medical Sciences L.A. Durnov
23 Kashirskoe Shosse, Moscow, 115522
A. Z. Dzampaev
Russian Federation
Cand. of Sci. (Med.), Pediatric Oncologist Pediatric Oncology Department of Surgical Methods of Treatment No. 2 (Tumors of Thoracoabdominal Localization and Musculoskeletal System) of the Research Institute of Pediatric Oncology and Hematology named after Academician of the Russian Academy of Medical Sciences L.A. Durnov
23 Kashirskoe Shosse, Moscow, 115522
S. R. Varfolomeeva
Russian Federation
Dr. of Sci. (Med.), Professor, Director of the Research Institute of Pediatric Oncology and Hematology named after Academician of the Russian Academy of Medical Sciences L.A. Durnov
23 Kashirskoe Shosse, Moscow, 115522
References
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Review
For citations:
Khestanov D.B., Efimova M.M., Romantsova O.M., Khairullova V.V., Malakhova A.A., Mikhailova E.V., Dzampaev A.Z., Varfolomeeva S.R. Synovial sarcoma of the median nerve of the right shoulder (case report). Russian Journal of Pediatric Hematology and Oncology. 2023;10(1):68-72. (In Russ.) https://doi.org/10.21682/2311-1267-2023-10-1-68-72